Anti-SGSH Antibody |产品详情|进口橙子视频旧款采购网

您好，欢迎来到橙子视频app安卓下载生物网站！请登录注册

我的订单 | 联系橙子视频app安卓下载 | 在线客服QQ：3012681483 | 客服电话：400-968-7988 | 工作时间：08:30-17:30

主营产品： ELISA91橙子视频、抗体、补体血清、兔补体、干扰素、小鼠测温仪、进口橙子视频旧款、Quidel代理、Swant代理、PBL Assay Science代理

网站首页产品中心代理品牌新闻资讯资源中心关于橙子视频app安卓下载

所在位置：首页 > 产品中心 > Antibodies > Antibodies产品

订购信息

上海橙子视频app安卓下载生物科技公司

Tel:400-968-7988 021-33779008

Anti-SGSH Antibody

品牌：Antibodies

货号：

规格：50µl

货期：

应用：

咨询客服

立即购买加入购物车

Anti-SGSH Antibody

商品详情参考文献相关资料

Overview

Name:	Anti-SGSH Antibody See all SGSH primary antibodies
Description:	Rabbit polyclonal antibody to SGSH.
Applications:	WB, IHC
Dilutions:	WB: 1:500 - 1:2000, IHC: 1:50 - 1:100.
Reactivity:	Human
Immunogen:	Recombinant protein of human SGSH.
Protein Length:	502
Host:	Rabbit
Clonality:	Polyclonal
Isotype:	IgG
Conjugate:	Unconjugated
Purification:	Affinity purification.
Product Form:	Liquid
Formulation:	Supplied in Phosphate Buffered Saline, pH 7.30, with 0.02% Sodium Azide and 50% Glycerol.
Storage:	Shipped at 4°C. Upon delivery aliquot and store at -20°C. Avoid freeze / thaw cycles.

Target

Function:	Catalyzes a step in lysosomal heparan sulfate degradation.
Involvement in Disease:	Mucopolysaccharidosis 3A: A severe form of mucopolysaccharidosis type 3, an autosomal recessive lysosomal storage disease due to impaired degradation of heparan sulfate. MPS3 is characterized by severe central nervous system degeneration, but only mild somatic disease. Onset of clinical features usually occurs between 2 and 6 years; severe neurologic degeneration occurs in most patients between 6 and 10 years of age, and death occurs typically during the second or third decade of life. MPS3A is characterized by earlier onset, rapid progression of symptoms and shorter survival.
Sequence Similarities:	Belongs to the sulfatase family.
Post-Translational Modification:	The conversion to 3-oxoalanine (also known as C-formylglycine, FGly), of a serine or cysteine residue in prokaryotes and of a cysteine residue in eukaryotes, is critical for catalytic activity.
Cellular locations:	Lysosome.
Database Links:	Entrez Gene: 6448?Human Omim: 605270?Human SwissProt: P51688?Human Unigene: 31074?Human
Synonyms:	Heparan sulfate sulfatase Antibody Heparan sulphate sulphatase Antibody HSS Antibody MPS 3A Antibody MPS3 A Antibody MPS3A Antibody Mucopolysaccharidosis type IIIA Antibody N sulfoglucosamine sulfohydrolase Antibody N sulfoglucosamine sulfohydrolase (sulfamidase) Antibody N-sulphoglucosamine sulphohydrolase Antibody SFMD Antibody SGSH Antibody SPHM_HUMAN Antibody Sulfoglucosamine sulfamidase Antibody Sulphamidase Antibody Sulphoglucosamine sulphamidase Antibody
Information:	Target information shown above is from the UniProt Consortium.